Ovarian Localization of a Peripheral Primitive Neuroectodermal Tumor: Definitive Diagnosis is a Real Challenge

Primary neuroectodermal tumors (PNET) are aggressive tumors composed of small, round hyperchromic cells. Depending on their locations and the mother cell, they are classified into two subtypes: peripheral and central. Their locations in the genital tract are rare. We report here a case of peripheral primitive neuroectodermal tumor (pPNET) in the ovary, in a 42-year-old patient, whose definitive diagnosis was made on the basis of histological, immunohistochemical and molecular results.