This case demonstrates the clinical management of a complex hereditary pheochromocytoma with vascular invasion using surgical resection, IVC thrombectomy, and subsequent anticoagulation.
We report a case of bilateral pheochromocytomas in a 45-year-old man with cutaneous findings suggestive of a hereditary disease. Imaging revealed a large right adrenal tumor extending into the inferior vena cava (IVC) and a smaller contralateral lesion. The patient underwent right adrenalectomy with IVC thrombectomy, while the left lesion was managed conservatively. Histopathology confirmed pheochromocytoma with extensive IVC tumor thrombus and no distant metastases. A residual IVC thrombus was treated with anticoagulation and remained stable on follow-up imaging. This case highlights the complexity of managing hereditary pheochromocytomas with vascular invasion.
Chebbi et al. (Thu,) studied this question.