HSS is a life-threatening condition that must be considered in young patients with hemoptysis and thrombosis, particularly when clinical features are suggestive but incomplete for Behçet's disease. CT angiography is essential for diagnosis. Treatment centers on aggressive immunosuppression to halt aneurysm progression, requiring a delicate balance with anticoagulation. Endovascular intervention is often necessary for large aneurysms to prevent a fatal outcome.
Al-Bitar et al. (Tue,) studied this question.