Two cases of benign Duchenne type of progressive muscular dystrophy demonstrated myocardial involvement, characterized by a paradoxical systolic expansion of the posterolateral left ventricular wall.
Case Report (n=2)
Benign Duchenne muscular dystrophy can involve severe, localized myocardial damage in the posterolateral left ventricular wall, leading to specific ECG, VCG, and cineangiocardiographic abnormalities.
Two cases of benign Duchenne type of progressive muscular dystrophy with myocardial involvement were presented. In one case, congestive heart failure was the predominant clinical feature and severe impairment of the left ventricular function was demonstrated by hemodynamic and cineangiocardiographic studies. Analysis of the cineangiocardiogram demonstrated a systolic expansion of the posterolateral portion of the left ventricular wall in both cases, which corresponded to the site of severe myocardial damage of the left ventricle in one autopsied case. A possible relationship between the site of myocardial damage and electrocardiographic and vectorcardiographic abnormalities was also discussed.
Ueda et al. (Thu,) conducted a case report in Benign Duchenne type of progressive muscular dystrophy (n=2). Benign Duchenne type of progressive muscular dystrophy was evaluated on Myocardial involvement (clinical, hemodynamic, and cineangiocardiographic findings). Two cases of benign Duchenne type of progressive muscular dystrophy demonstrated myocardial involvement, characterized by a paradoxical systolic expansion of the posterolateral left ventricular wall.
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