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February 1, 1993HeartOpen Access

Right ventricular dysplasia: a clinical and pathological study of two families with left ventricular involvement.

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Population

8 patients from two families affected by right ventricular dysplasia

Design

Case_series

Authors

DMDaniela MianiBPBruno PinamontiRBRossana Bussani

Discussion

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Overview

LV involvement warrants consideration in familial RV dysplasia evaluation; challenges RV-selective view but case reports leave generalizability open.

Structured PICO

P
Population
8 patients from two families affected by right ventricular dysplasia (at least one member per family had necropsy-confirmed right ventricular dysplasia)
O
Outcome
Prevalence and characteristics of left ventricular involvement assessed by echocardiography, angiography, or necropsysurrogate

Familial right ventricular dysplasia frequently involves the left ventricle and can be progressive, potentially mimicking dilated cardiomyopathy in advanced stages.

Cite This Study

Miani et al. (1993) studied this question.

synapsesocial.com/papers/6a1970e0f9a68600c7d986b6https://doi.org/10.1136/hrt.69.2.151
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