Fibromuscular dysplasia (FMD) is a noninflammatory vascular disease that predominantly affects women. A 42-year-old man with progressive claudication presented with superficial femoral artery occlusion, tortuous coronary arteries, and radial artery involvement. Histopathology confirmed FMD despite atypical sex and vascular distribution. FMD must be considered in young men with nonatherosclerotic vascular disease. Multimodal imaging and biopsy are critical for diagnosis.
Koga et al. (Fri,) studied this question.
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