Double patch aortoplasty successfully treated severe supravalvular aortic stenosis in a 15-year-old girl with reduced ejection fraction and severe mitral regurgitation.
Double patch aortoplasty with bovine pericardium successfully treated severe supravalvular aortic stenosis in a 15-year-old girl, leading to sustained functional and echocardiographic improvement over 2 years.
Absolute Event Rate: 0% vs 0%
ABSTRACT Severe supravalvular aortic stenosis in a young patient is a rare but critical condition requiring timely diagnosis and intervention. We report a 15‐year‐old girl presenting with exertional dyspnea, chest pain, and palpitations. Echocardiography and multidetector computed tomography (MDCT) confirmed severe supravalvular aortic stenosis, myxomatous mitral valve with moderate to severe mitral regurgitation, and reduced ejection fraction. A double patch aortoplasty was performed with a successful outcome. This case underscores the importance of early diagnosis and tailored surgical intervention along with continued monitoring during follow up visits in managing complex congenital heart disease (CHD) diagnosed at an early age.
Kadel et al. (Fri,) reported a other. Double patch aortoplasty successfully treated severe supravalvular aortic stenosis in a 15-year-old girl with reduced ejection fraction and severe mitral regurgitation.