Multimodality imaging in a child with complete atrioventricular canal defect, left superior vena cava, and airway compression: Echocardiography, bronchoscopy, and lung ultrasound insights

Key Points

• To demonstrate the importance of multimodality imaging for diagnosis and management of congenital heart disease and airway abnormalities.
• Conducted transthoracic echocardiography to confirm atrioventricular canal defect and pulmonary hypertension.
• Preoperative computed tomography assessed airway compression and bronchial abnormalities.
• Performed intraoperative bronchoscopy to evaluate left bronchomalacia.
• Employed transesophageal echocardiography to identify coronary sinus dilation.
• Utilized lung ultrasound to check for lung collapse pre-extubation.
• Echocardiography confirmed atrioventricular canal defect, left superior vena cava, and severe pulmonary hypertension.
• Computed tomography revealed left pulmonary artery compression and potential cor triatriatum.
• Bronchoscopy found left bronchomalacia but excluded cor triatriatum based on echocardiographic findings.
• Surgical intervention involved repairing the atrioventricular canal defect and connecting the left superior vena cava to the right atrial appendage.
• Postoperative echocardiography indicated no residual regurgitation or inflow gradient, and lung ultrasound showed no left lung collapse.

Abstract