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This research focuses on the feasibility and outcomes of surgical repair for late-presenting total anomalous pulmonary venous connection.

May 24, 2026Open Access

Surgical repair of extremely late presentation of supracardiac total anomalous pulmonary vein connection: a case series

Key Points

This research focuses on the feasibility and outcomes of surgical repair for late-presenting total anomalous pulmonary venous connection.
Presented two cases of surgical repair for supracardiac total anomalous pulmonary vein connection.
Patients included a 14-year-old female and a 32-year-old female.
Monitored postoperative recovery, including complications and heart function.
Both patients were successfully operated on and discharged after 9 and 29 days respectively.
The second patient experienced acute kidney injury requiring hemodialysis.
Postoperative evaluations showed no pulmonary vein obstruction and normal biventricular contraction.

Abstract

BACKGROUND: A late-presenting total anomalous pulmonary venous connection is extremely rare, and surgical repair remains a significant challenge. CASES PRESENTATION: We present two cases of surgical repair for late-presenting supracardiac total anomalous pulmonary vein connection: a 14-year-old female and a 32-year-old female. Both were successfully operated on and were discharged on postoperative days 9 and 29. The second patient had a prolonged hospital stay due to complications of acute kidney injury after surgery and the need for hemodialysis. Both patients had a small left ventricle and pulmonary hypertension preoperatively. All pulmonary veins drained to a common pulmonary vein, which drained to a left-sided vertical vein, which drained into the innominate vein. Postoperative evaluation of both patients found no pulmonary vein obstruction and good biventricular contraction. CONCLUSION: Late diagnosis may occur in TAPVC patients, but a surgical repair may still be possible.

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