In 11 young patients with myotonic dystrophy type 1, major cardiac rhythm disturbances were observed, with physical exercise acting as a prominent arrhythmogenic factor.
Observational (n=11)
Young patients with myotonic dystrophy type 1 can experience major cardiac rhythm disturbances, particularly exercise-induced tachyarrhythmias, suggesting a potential need for systematic exercise testing with EKG monitoring.
Cardiac tachyarrhythmias have rarely been studied in young patients with myotonic dystrophy type 1 (DM1). The authors observed major cardiac rhythm disturbances in 11 patients aged 10 to 18 years. Tachyarrhythmic events were more frequent than impulse conduction disorders. Wide variations in CTG expansion were observed among the population. Since physical exercise was a prominent arrhythmogenic factor, systematic exercise tests with EKG monitoring may be indicated in young patients with DM1.
Bassez et al. (Tue,) conducted a observational in Myotonic dystrophy type 1 (DM1) (n=11). Myotonic dystrophy type 1 (DM1) was evaluated on Major cardiac rhythm disturbances. In 11 young patients with myotonic dystrophy type 1, major cardiac rhythm disturbances were observed, with physical exercise acting as a prominent arrhythmogenic factor.