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An infant with a newly-described subtype of congenital long QT syndrome is presented, along with her perioperative management on three separate occasions. During each anaesthetic characteristic arrhythmias occurred. The available literature and rational approaches to these high risk patients are reviewed.
Joseph-Reynolds et al. (1997) studied this question. Anaesthesia in an infant with a newly described subtype of congenital long QT syndrome consistently provoked characteristic arrhythmias during three separate perioperative events.