Chiari’s Syndrome

CHIARI'S syndrome is a rarely observed clinical entity and is seldom diagnosed during life. It was first adequately described by Budd1 in 1846 but bears the name of Chiari,2 who in 1899 reported more completely 3 cases seen in his clinic and collected 7 additional cases. As first described the syndrome was a manifestation of a primary obliterating endophlebitis of the hepatic veins. Other related pathologic processes have subsequently been shown to produce this disease entity.The symptom complex manifested by this syndrome is not generally known. A search of the literature reveals only about 70 reported cases. Out of . . .