An 11-year-old male with bidirectional ventricular tachycardia and a combined phenotype of nonhypertrophic hypertrophic cardiomyopathy and prolonged QTU interval was successfully treated with phenytoin and an ICD.
Case Report (n=1)
This case highlights a rare presentation of bidirectional ventricular tachycardia caused by a combined phenotype of nonhypertrophic hypertrophic cardiomyopathy and channelopathy, which proved uniquely responsive to phenytoin.
Bidirectional ventricular tachycardia (BDVT), a rare ventricular arrhythmia, is commonly caused by digitalis toxicity or channelopathies and is rarely caused by aconite toxicity, myocarditis, infarction, or sarcoidosis. This paper describes a patient with BDVT, recurrent syncope, myocardial disarray, and interstitial fibrosis on histology but normal results on echocardiography with variants in the TTN, KCNH2, and GATA4 genes. (Level of Difficulty: Advanced.)
Chakraborty et al. (Sat,) conducted a case report in Bidirectional ventricular tachycardia (n=1). Phenytoin and implantable cardioverter-defibrillator was evaluated. An 11-year-old male with bidirectional ventricular tachycardia and a combined phenotype of nonhypertrophic hypertrophic cardiomyopathy and prolonged QTU interval was successfully treated with phenytoin and an ICD.
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