Clinical phenotype and long-term damage in paediatric Behçet’s disease: comparative performance of ISG, ICBD and PEDBD classification criteria in a retrospective endemic cohort

Key Points

• This research aims to compare the performance of ICBD, ISG, and PEDBD classification criteria in pediatric Behçet’s disease and assess long-term damage.
• Retrospective analysis of a cohort with pediatric Behçet’s disease
• Comparison of classification criteria: ICBD, ISG, and PEDBD
• Assessment of morbidity related to neurovascular events and ocular disease
• ICBD showed superior sensitivity compared to ISG and PEDBD
• ISG and PEDBD classified only 50% of cases
• Morbidity associated mainly with neurovascular events, less frequently with ocular disease

Abstract