Generalized Cutaneous Neurofibromatosis type-1 with Plexiform involvement: A Clinical Image

A 68- year- old female, presented to the hospital with complaint of swelling and pain in anterior neck along with long standing, progressively increasing multiple skin lesions since early adulthood. On examination, numerous soft, skin coloured to hyperpigmented papules and nodules of varying size ranging from 3mm to more than 3cm distributed diffusely over neck, face, trunk, and upper extremities consistent with neurofibromas (figure 1a). In Addition, multiple well defined hyperpigmented macules were noted over axilla and trunk(figure1b,1c). A large, lobulated, pendulous mass involving chin and anterior neck region was observed, consistent with plexiform neurofibroma