Congenital unilateral absence of the vas deferens

Introduction: A 65-year-old male with a known history of unilateral renal agenesis was found to have concurrent absence of the vas deferens ipsilaterally. Case Report: The patient presented with organic erectile dysfunction and wanted to proceed with surgical management. Routine pre-operative evaluation confirmed history of a left solitary kidney, and physical exam revealed absence of the right vas deferens. Previous imaging confirmed right renal agenesis, and with subsequent absence of the right vas deferens noted on physical exam, this confirmed embryological arrest as the cause of the anatomic abnormality. Conclusion: Congenital unilateral absence of the vas deferens (CUAVD) is an uncommon finding that is largely found during infertility evaluations and vasectomy consults. It is important to understand genetic components and embryological origins of CUAVD to appropriately evaluate patients for additional defects.