Surgical resection was performed in a 25-year-old man to treat exceptionally rare synchronous fibromatosis involving the right atrium and right pulmonary artery.
Case Report (n=1)
Cardiac fibromatosis is an exceptionally rare condition that can present with severe hemodynamic compromise and may be associated with prior cardiac surgery.
A 25-year-old man presented with severe hemodynamic compromise manifesting as superior vena cava (SVC) syndrome, inferior vena cava (IVC) syndrome and right pulmonary artery occlusion. Multimodality imaging revealed two separate, noncontiguous lesions involving the right atrium and distal right pulmonary artery. The patient underwent surgical resection, and postoperative histopathology confirmed fibromatosis. Cardiac fibromatosis is exceptionally rare and, in this case, may be associated with an atrial septal defect (ASD) repair performed eight years earlier.
Zhai et al. (Sun,) conducted a case report in Synchronous Fibromatosis (n=1). Surgical resection was evaluated. Surgical resection was performed in a 25-year-old man to treat exceptionally rare synchronous fibromatosis involving the right atrium and right pulmonary artery.