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February 12, 2026JACC Case Reports1 citationsOpen Access

Pentalogy of Cantrell

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JAJosé Martín Alanís-NaranjoJCJavier De la Cruz-PelayoRMRegina de la Mora-Cervantes

Key Points

  • To investigate the presentation and management complexities of Pentalogy of Cantrell in adult patients.
  • Utilized multimodal imaging techniques for diagnosis.
  • Assessed severity of intracardiac and thoracoabdominal defects.
  • Analyzed management approaches based on defect severity.
  • PC rarely presents in adulthood.
  • Survival is linked to less severe intracardiac and thoracoabdominal defects.
  • Effective imaging is crucial for better management outcomes.

Abstract

PC rarely presents in adulthood. Multimodal imaging is essential for diagnosis and management. Survival depends on less severe intracardiac and thoracoabdominal defects.

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Cite This Study

Alanís-Naranjo et al. (2026) studied this question.

synapsesocial.com/papers/698d6e2a5be6419ac0d53a8fhttps://doi.org/10.1016/j.jaccas.2026.106922
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