Background Pleuroparenchymal fibroelastosis (PPFE) is an upper lobe – predominant interstitial pneumonia pattern that can be idiopathic or secondary and has unclear clinical characteristics, disease course, and prognostic factors. This study analyzed PPFE patient characteristics, identified mortality predictors, and compared disease progression between idiopathic and secondary PPFE.
Baqir et al. (Fri,) studied this question.