Anesthesia in an Child with a Single Atrium: A Case Report and Review of the Literature

Single atrium is a rare congenital heart disease defined by a complete absence of the interventricular septum and endocardial cushion, an absence of ventricular septal defect, and an absence of atrioventricular valve malformations. Given the epidemiological, diagnostic, and therapeutic interest, and more specifically, anesthesiological management, we report a clinical case of a 9-month-old infant admitted for the treatment of stomal prolapse. The infant has several congenital malformations: a single atrium, an anorectal malformation, and hexadactyly of both thoracic and pelvic limbs. The paraclinical biological and biochemical assessments were normal. One intraoperative incident involving constant desaturation followed by cardiac arrest was reported, which progressed favorably without neurological sequelae.