Pseudo - Kaposi Sarcoma in a Young Obese Male

Pseudo-Kaposi sarcoma (PKS) or Acroangiodermatitis (AAD) is a rare disease that is sometimes difficult to distinguish clinically and histologically from Kaposi sarcoma and includes two entities: Acroangiodermatitis of Mali which is associated with chronic venous insufficiency and occurs in old age, and, Stewart Blefarb and Adams syndrome (SBS) which occurs in younger people and is conditioned by arterio-venous malformations. Here is presented a young (31 years old), obese (120 kg) man with erythemo-brownish plaques in the lower legs that last for 4 years. Histopathological verification indicated lobular proliferation of capillaries and small lymphatics in the dermis. The perivascular infiltrate consisted of histiocytes, lymphocytes. Immunohistochemically, CD34 staining was positive in vascular endothelium and negative in interstitium cells.Staining for HHV8 was negative. The correlation of the clinical and immunohistological picture indicated Acroangiodermatitis of Mali.