This case illustrates treatment challenges and outcomes of a neglected dermatofibrosarcoma protuberans patient, highlighting diagnostic delays and multidisciplinary management.
Background: Dermatofibrosarcoma protuberans is a rare soft-tissue sarcoma. Diagnostic delays in primary care often lead to extensive tissue damage. This report illustrated the clinical course and management challenges of a neglected tumor at a community health center. Case Presentation: A 50-year-old laundry worker presented in February 2024 with a 3-year history of right upper back pain and a violaceous, firm nodule (3 × 2 × 1 cm) previously treated by traditional healers. Radiographs excluded bone involvement. Excisional biopsy confirmed DFSP with fibrosarcomatous features. In April 2024, wide excision with 2 cm margins achieved clear histologic borders. From May 2024 to January 2025, she received adjuvant radiotherapy (35 × 2 Gy), during which skin blistering and infection were managed with bi-daily wound care. A surveillance CT in January 2025 showed stable necrotic changes and no metastases. Persistent shoulder pain and restricted mobility prompted physiotherapy. Discussion: Dermatofibrosarcoma protuberans (DFSP) is a rare, indolent sarcoma whose delayed recognition in primary care—as illustrated here—necessitated wide excision and radiotherapy, underscoring the value of early diagnosis and a coordinated, multidisciplinary treatment strategy. Post‐treatment physiotherapy targeting shoulder pain was essential to restore function, improve mobility, relieve pain, and optimize the patient’s quality of life. Conclusion: Early recognition of atypical cutaneous lesions, structured referral pathways, and a multidisciplinary approach are essential in resource-limited settings. Enhanced training for general practitioners and integration of surgical, oncologic, radiotherapeutic, and rehabilitative services can reduce diagnostic delays and optimize functional recovery.
No takes yet. Share an insight, caveat, or question.
Fathaniy et al. (2025) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: