Wolf-Hirschhorn syndrome (WHS) is a rare genetic disorder caused by 4p chromosome microdeletion, characterized by distinctive craniofacial features, growth delay, short stature and slow height gain, variable degrees of intellectual disabilities, epilepsy, and congenital heart disease. Anesthetic management in pediatric patients with WHS requires a tailored approach due to the complex multisystem involvement, and the optimal strategy remains undetermined despite several published case reports. We present the airway management of an eight-year-old patient with WHS undergoing strabismus surgery using a supraglottic device. Although our patient's distinctive craniofacial features of WHS suggested a potential for difficult intubation; after mitigating the risk of aspiration, a flexible laryngeal mask was successfully placed on the first attempt, offering a viable alternative to the challenges of tracheal intubation.
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Gholmieh et al. (2024) studied this question.
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