Síndrome de Caroli: un caso en el segundo nivel de atención

Caroli's syndrome or disease is a rare pathology that affects the intrahepatic bile ducts and presents with various complications, such as cholangitis, portal hypertension and the fearsome cholangiocarcinoma.This is the case of a male patient with a diagnosis of Caroli's syndrome who was admitted to the internal medicine service due to decompensated cirrhosis, hepatic encephalopathy, cholangitis, spontaneous peritonitis and hepatorenal syndrome.