A Rare Case of Subconjunctival Nerve Sheath Myxoma Presenting as Orbital Fat Prolapse

Nerve sheath myxomas are extremely rare myxoid peripheral nerve sheath tumors with a predilection for the distal extremities, particularly common in the fingers and knees. Here, the authors report a 60-year-old male patient with a subconjunctival epibulbar nerve sheath myxoma, which was clinically diagnosed as an orbital fat prolapse. The lesion was successfully debulked without clinical recurrence over more than 3 years. To the authors’ knowledge, this is the first case with subconjunctival presentation and fourth orbital reported case.