Case Report: Diagnosing and Treating a 11 Year Old Girl with Herlyn-werner-wunderlich Syndrome

Introduction:The Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly characterized by uterus didelphys, obstructed hemivagina and mesonephric duct anomalies.Most often the later manifests as renal agenesis [1].Incidence of thisThe patient is usually asymptomatic in early childhood, onset of symptoms occur after menarche and common complaints are progressive dysmenorrhea, recurrent pain abdomen and palpable lump over lower abdomen.Patient can also present with urinary problems like recurrent UTI, vesico-ureteric reflux, increased risk of hypertension, compensatory hypertrophy of existing kidney, in severe cases Chronic Kidney Disease CKD and End Stage Renal Disease ESRD that occur as complication of unilateral solitary kidney.Case Report: Case report presented here is of an 11 year old girl who presented with pain lower abdomen and pelvic region, fever, palpable tender mass over right lower abdomen and urinary complaints.Further evaluation of the case with biochemical parameters and radiological modalities like Ultrasound (USG) and Magnetic Resonance Imaging (MRI) confirmed the diagnosis as HWW syndrome complicated with CKD after which surgical management of the case was followed. Conclusion: Duplication of the uterus and cervix with obstructed hemivagina and iplsilateral renal agenesis (presence of both) should prompt the clinicians to think in the direction of HWW syndrome.Early diagnosis and prompt treatment of the condition can prevent possible serious complication in future.