Triple Century in a Century (Lhermitte–Duclos Disease) -The Tale of a CNS Tumor (P6-5.002)

Dysplastic cerebellar gangliocytoma (DCG) is an extremely rare tumor with nearly 300 reported cases since 1920. We intend to generate awareness about 1. Presentation-slow growth, posterior fossa location, pressure effects & spatial heterogeneity (non-concentrated and multifocal involvement) with recurrence potential, 2. Genetic testing and cancer surveillance for its relation to Cowden syndrome.