Case report demonstrates effective coil embolisation of a hepatic artery aneurysm in a patient with vascular ehlers-danlos syndrome, highlighting challenges and innovative solutions.
Background Vascular Ehlers–Danlos syndrome is a rare connective tissue disorder characterised by arterial fragility, predisposing patients to life-threatening vascular complications. Endovascular aneurysm management in these individuals poses significant challenges due to their delicate vasculature and limited surgical options. This case report highlights the novel use of a direct percutaneous transhepatic approach for aneurysm coiling in a patient with a rapidly expanding hepatic artery aneurysm, demonstrating an innovative solution to a complex vascular emergency. Case presentation A 17-year-old male with a known diagnosis of vascular Ehlers–Danlos syndrome presented with a perforated sigmoid colon. After undergoing a midline exploratory laparotomy, imaging revealed a rapidly expanding 50-mm aneurysm in his common hepatic artery. Traditional endovascular coiling was infeasible due to significant proximal stenosis, creating similar limitations for vascular reconstruction and liver transplantation. The multidisciplinary team opted for a direct transhepatic approach to coil the aneurysm. The patient recovered without complications, and follow-up imaging confirmed haemodynamic stability and adequate liver perfusion. Conclusions This case highlights the importance of an integrative multidisciplinary approach in managing complex vascular emergencies and successfully demonstrates how a direct percutaneous transhepatic approach can serve as a valuable reference for similar cases, expanding the repertoire of endovascular interventional radiology techniques for challenging pathologies.
No takes yet. Share an insight, caveat, or question.
Chan et al. (2025) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: