Case report demonstrates effective dental management in a child with epidermolysis bullosa simplex, suggesting the need for early referral and multidisciplinary care.
Oral healthcare is severely hampered in patients with epidermolysis bullosa simplex (EBS), a rare inherited genodermatosis marked by mucocutaneous fragility and blister formation. This case report describes the dental management of a six-year-old female child clinically diagnosed with EBS presenting with severe periodontal manifestations such as extensive calculus accumulation, gingival bleeding, halitosis, and poor oral hygiene as a result of frequent oral ulcerations. Meticulous behaviour modification technique and atraumatic periodontal intervention were employed to minimize soft tissue injury. This report highlights the importance of early dental referral, preventive-focused care, and a multidisciplinary approach in managing pediatric patients with EBS.
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Duff et al. (2026) studied this question.
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