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March 21, 2026Annals of Neurology3 citationsOpen Access

The Dynamics of Neurofilament Light Chain in Spinal Muscular Atrophy

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ADArlene D'SilvaKHKaren HerbertLBLakshmi Balaji

Key Result

Serum neurofilament light chain provides early insights into pathophysiology prior to clinical phenotypes in spinal muscular atrophy, potentially expediting treatment initiation.

Key Points

  • The aim is to investigate the role of neurofilament light chain levels in understanding spinal muscular atrophy dynamics in children.
  • Analyzed neurofilament light chain levels in children with spinal muscular atrophy
  • Focused on patients with 2 SMN2 copies
  • Examined correlations with disease progression and denervation
  • Found elevated neurofilament light chain levels in patients prior to clinical symptoms
  • Indicated that sNfL can provide early insights into disease progression
  • Suggests that monitoring sNfL may expedite treatment initiation

Structured PICO

Does sNfL assessment provide early insights into pathophysiology prior to clinical phenotype in neonates with Spinal Muscular Atrophy and 2 SMN2 copies?

P
Population
Children with Spinal Muscular Atrophy and 2 SMN2 copies within the neonatal period
I
Intervention
sNfL (serum Neurofilament Light Chain) assessment
O
Outcome
Early insights into underlying pathophysiology prior to a clinical phenotypesurrogate

sNfL assessment in neonates with SMA and 2 SMN2 copies may provide early pathophysiological insights and expedite treatment initiation.

Abstract

There is a malignant disease course with active denervation in children with 2 SMN2 copies within the neonatal period. sNfL gives early insights into underlying pathophysiology prior to a clinical phenotype and may expedite access to the initiation of treatment. ANN NEUROL 2026.

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Cite This Study

D'Silva et al. (2026) studied this question. Serum neurofilament light chain provides early insights into pathophysiology prior to clinical phenotypes in spinal muscular atrophy, potentially expediting treatment initiation.

synapsesocial.com/papers/69be386a6e48c4981c678c83https://doi.org/10.1002/ana.78207
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