Pleuropulmonary synovial sarcoma is a distinct, aggressive anatomic subset of synovial sarcoma.
The authors conclude that pleuropulmonary SS, although rare, represents a distinct anatomic subset having pathologic features similar to those of its soft tissue counterpart. Its clinical behavior appears more aggressive, perhaps because of relatively later presentation combined with the difficulty in obtaining a wide surgical margin.
Essary et al. (Tue,) studied this question.