A tricuspid valve papillary fibroelastoma in a pediatric patient: an atypical presentation of a benign cardiac tumor

Q: What is the clinical evidence from this study?

Study design: Case Report. Population: Tricuspid valve papillary fibroelastoma (n=1). Intervention: Surgical resection and valve reconstruction. Primary outcome: Post-operative clinical and echocardiographic status.

Pliceliany Perez-Kersey; Surbhi Gupta; Carol McFarland; Samuel Keller; Megan M Vernon; Addison Gearhart

doi:10.5348/100153z10pk2026cr

March 31, 2026Journal of Case Reports and Images in OncologyOpen Access

A tricuspid valve papillary fibroelastoma in a pediatric patient: an atypical presentation of a benign cardiac tumor

View Full Paper

Ask AI

Bookmark

Share

Why the study?

Papillary fibroelastoma is a rare benign cardiac tumor typically seen in adults and located on the left side of the heart.

Key Points

To describe the atypical clinical presentation, multimodal diagnostic imaging, and surgical management of a right-sided cardiac papillary fibroelastoma in a young child.
Evaluated an asymptomatic 2-year-old female referred for a harsh III/VI holosystolic murmur using transthoracic echocardiography and cardiac magnetic resonance imaging.
Conducted surgical resection of the tricuspid valve mass with autologous pericardial reconstruction and histopathologic assessment.
Echocardiography and cardiac magnetic resonance imaging demonstrated a mobile mass attached to the tricuspid valve causing mild-to-moderate eccentric tricuspid regurgitation.
Intraoperative inspection revealed a 26 × 17 × 15 mm multi-lobular polypoid mass originating from the septal leaflet near the anteroseptal commissure.
Histopathology confirmed avascular fibroelastic tissue surrounded by endocardium diagnostic of papillary fibroelastoma, and the patient remained asymptomatic with normal valve function at follow-up.

Study Design

Type

Case Report (n=1)

Multicenter

No

Structured PICO

P

Population

1 asymptomatic 2-year-old female referred for evaluation of a harsh III/VI holosystolic murmur, found to have a large mobile heterogenous echogenic mass attached to the tricuspid valve.

I

Intervention

Surgical resection of the mass and tricuspid valve reconstruction using autologous pericardium.

O

Outcome

Post-operative valve function and patient symptom status at follow-up.

Reports a rare case of a right-sided papillary fibroelastoma causing valvular dysfunction in a 2-year-old child, successfully treated with surgical resection.

Ask about this paper

Answers are grounded in this paper and cite their sources.

Implication

Consider in differential for pediatric harsh holosystolic murmurs; extends known papillary fibroelastoma spectrum to young children and right-sided valves.

Abstract

Papillary fibroelastoma is a rare benign cardiac tumor typically seen in adults and when present is on the left side of the heart. We present the case of an otherwise healthy 2-year-old female referred to cardiology for a harsh holosystolic found to have a papillary fibroelastoma involving the tricuspid valve.

Discussion

No takes yet. Share an insight, caveat, or question.

Cite This Study

Perez-Kersey et al. (2026) conducted a case report in Tricuspid valve papillary fibroelastoma (n=1). Surgical resection and valve reconstruction was evaluated on Post-operative clinical and echocardiographic status.

synapsesocial.com/papers/69e713decb99343efc98d48d https://doi.org/10.5348/100153z10pk2026cr

View Full Paper

Ask AI

Bookmark

Share

A tricuspid valve papillary fibroelastoma in a pediatric patient: an atypical presentation of a benign cardiac tumor

Key Points

Study Design

Structured PICO

Ask about this paper

Implication

Abstract

Discussion

Cite This Study

A tricuspid valve papillary fibroelastoma in a pediatric patient: an atypical presentation of a benign cardiac tumor

Key Points

Study Design

Structured PICO

Ask about this paper

Implication

Abstract

Discussion

Cite This Study

Keep reading

Keep reading