Why the study?
Although ARVC is rare, many patients are disproportionately referred for cardiac MRI, prompting a review of magnetic resonance characteristics and recent improvements not included in the 2010 Task Force criteria.
What are the cardiac magnetic resonance imaging characteristics of arrhythmogenic right ventricular cardiomyopathy in adults and children?
What are the cardiac magnetic resonance imaging characteristics of arrhythmogenic right ventricular cardiomyopathy in adults and children?
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This review summarizes the key cardiac MRI features of ARVC and highlights recent diagnostic criteria improvements that may inform future guidelines.
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare disease in which the right ventricular myocardium is replaced by islands of fibro-adipose tissue. Therefore, ventricular re-entry circuits can occur, predisposing the patient to ventricular tachyarrhythmias, as well as dilation of the right ventricle that eventually leads to heart failure. Although it is a rare disease with low prevalence in Europe and the United States, many patients are addressed disproportionately for cardiac magnetic resonance imaging (MRI). The most severe consequence of this condition is sudden cardiac death at a young age due to untreated cardiac arrhythmias. The purpose of this paper is to revise the magnetic resonance characteristics of ARVC, including the segmental contraction abnormalities, fatty tissue replacement, decrease of the ejection fraction, and the global RV dilation. Herein, we also present several recent improvements of the 2010 Task Force criteria that are not included within the ARVC diagnosis guidelines. In our opinion, these features will be considered in a future Task Force Consensus.
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Căinap et al. (2021) studied this question.
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