Key result
Transapical myectomy successfully treats a child with apical HCM in a Russian first.
Why the study?
There is little information on the treatment of apical HCM in the pediatric population, where heart transplantation is typically preferred.
Case Report (n=1)
No
Transapical myectomy is a feasible surgical option for pediatric patients with apical hypertrophic cardiomyopathy, potentially avoiding the need for heart transplantation.
May support transapical myectomy in pediatric apical HCM; leaves open need for prospective validation before wider use.
Apical hypertrophic cardiomyopathy (HCM) is a rare morphological variant (1—10%), in which hypertrophy is localized primarily in the apex of the left ventricle (LV). Patients with apical HCM have progressive intractable diastolic heart failure with severe symptoms that result from reduced LV volume and cardiac output. For a long time, the only treatment option for this form of hypertrophy in adults was heart transplantation. Currently, transapical myectomy in adults has proven itself to be an effective method adequately increasing LV cavity and cardiac output in early and late postoperative period. For pediatric population, there is a little information on the treatment of apical HCM, and heart transplantation is preferred in most cases. This clinical case describes the first successful experience of transapical myectomy in a child with apical type of HCM in the Russian Federation.
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Kozhanov et al. (2025) conducted a case report in Apical hypertrophic cardiomyopathy (n=1). Transapical myectomy was evaluated. Transapical myectomy was successfully performed in a child with apical hypertrophic cardiomyopathy, representing the first such experience in the Russian Federation.
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