Key result
Interventional electrophysiology provides overlapping treatment options for inherited arrhythmia syndromes, which are electrical myopathies with genetic origins and risk of sudden death.
This article reviews interventional electrophysiology options for managing inherited arrhythmia syndromes.
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May guide EP interventions in select inherited arrhythmia syndromes; leaves open need for prospective outcome data.
I Inherited arrhythmia syndromes are electrical myopathies with genetic origins and risk of sudden death.They may present from infancy through adulthood, although the specific diseases have stereotypic but variable phenotypic onset and severity.There is clinical and genetic overlap among the syndromes, with variable penetrance and expressivity.Although underlying mechanisms of arrhythmogenesis may differ between syndromes, the electrophysiological (EP), pharmacological, and interventional options overlap.Specifics of the genetics, pharmacological therapies, and lifestyle modifications have been reviewed recently and are beyond the scope of this article, which focuses on interventional electrophysiology for inherited arrhythmias.
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Stephenson et al. (2007) conducted a review in Inherited arrhythmia syndromes. Interventional electrophysiology was evaluated. Interventional electrophysiology provides overlapping treatment options for inherited arrhythmia syndromes, which are electrical myopathies with genetic origins and risk of sudden death.
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