Two-stage total aortic replacement successfully treated aortic root, arch, and thoracoabdominal pathology in a young man with Loeys-Dietz syndrome.
Demonstrates the feasibility of two-stage total aortic replacement for extensive aortopathy in a patient with Loeys-Dietz syndrome.
Absolute Event Rate: 0% vs 0%
Loeys-Dietz syndrome (LDS) is a recently described connective tissue disorder characterized by generalized arterial tortuosity and aggressive aortopathy that untreated leads to early death even at aortic dimensions as small as 4 cm. We report the case of a young man with LDS successfully treated for aortic root, arch, and thoracoabdominal pathology.
Williams et al. (Mon,) reported a other. Two-stage total aortic replacement successfully treated aortic root, arch, and thoracoabdominal pathology in a young man with Loeys-Dietz syndrome.