Key result
Surgical resection of a right atrial rhabdomyoma in a newborn presenting with frequent supraventricular extrasystoles resulted in complete resolution of the arrhythmia over a 6-year follow-up.
Case Report (n=1)
No
Frequent supraventricular extrasystoles in a newborn can be an early clinical presentation of a cardiac rhabdomyoma, which may not be initially visible on echocardiography.
Suggests evaluating for occult rhabdomyoma in refractory neonatal extrasystoles; hypothesis-generating from single case, needs prospective validation.
We are reporting the case of a newborn with a diagnosis of frequent supraventricular extrasystoles, up to 25% of beats at Holter monitoring, and partial response to beta-blockers. Initial echocardiographic studies were normal until the identification of a right atrial mass at 4 months of life. Given the progressive growth of the mass and the suspicion of myxoma or thrombus in the magnetic resonance study, surgical resection of the tumor was performed. The surgical specimen was histologically diagnostic of rhabdomyoma. Currently, the patient remains asymptomatic after a 6-year follow-up period. A single rhabdomyoma is described, located in an atypical situation, near the crista terminalis, and diagnosed from frequent extrasystoles which appeared before the echocardiographic resolution was able to identify it. Magnetic resonance showed nondiagnostic tissue enhancement characteristics.
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Esmel-Vilomara et al. (2018) conducted a case report in Cardiac rhabdomyoma (n=1). Surgical resection was evaluated on Resolution of extrasystoles and asymptomatic survival. Surgical resection of a right atrial rhabdomyoma in a newborn presenting with frequent supraventricular extrasystoles resulted in complete resolution of the arrhythmia over a 6-year follow-up.
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