Key result
This review presents current knowledge on the definition, prevalence, pathophysiology, classification, diagnosis, and treatment of pulmonary arterial hypertension related to congenital heart disease.
This review summarizes current knowledge on the definition, prevalence, pathophysiology, classification, diagnosis, and treatment of pulmonary arterial hypertension related to congenital heart disease.
Does not change PAH-CHD practice; leaves open needs for prospective validation of strategies.
The number of patients with pulmonary arterial hypertension related to congenital heart disease ( PAH ‐ CHD ) seen in specialist centers continues to increase. The extreme end of the spectrum, namely Eisenmenger's syndrome, is further compromised with chronic cyanosis and multiorgan disease, In this review we present the current knowledge on definition, prevalence, pathophysiology, classification, diagnosis, and treatment of this entity that has great impact on CHD patients’ life.
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Frogoudaki et al. (2018) conducted a review in Pulmonary arterial hypertension in congenital heart disease. This review presents current knowledge on the definition, prevalence, pathophysiology, classification, diagnosis, and treatment of pulmonary arterial hypertension related to congenital heart disease.