Middle ear salivary gland choristoma (SGCh) is an exceptionally rare benign tumor characterized by middle ear malformations accompanied by unilateral conductive hearing loss. Early diagnosis remains particularly challenging, and surgical excision constitutes the primary therapeutic approach. We present a 13-year-old male with congenital hearing impairment diagnosed with SGCh and surgically managed. This report describes the first documented case of SGCh coexisting with middle ear lipoma, analyzing its clinical presentation, imaging differential diagnostic challenges, and surgical management strategy to advance precise diagnostic and therapeutic interventions.
Chen et al. (2026) studied this question.