Key result
Short QT syndrome is a hereditary channelopathy characterized by short QT intervals and a high risk of sudden cardiac death, for which ICDs and quinidine are potential therapies.
Population
Infants, children, or young adults with hereditary short QT syndrome and a strong positive family background…
Design
Review
Authors
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Recognition of short QT ECG pattern may flag high-risk patients with normal hearts; leaves open optimal therapy selection pending prospective data.
Clinicians need to be aware of the short QT syndrome ECG pattern as it portends a high risk of sudden cardiac death in otherwise healthy subjects with structurally normal hearts.
Pérez‐Riera et al. (2005) conducted a review in Short QT Syndrome and Other Cardiac Channelopathies. Short QT syndrome is a hereditary channelopathy characterized by short QT intervals and a high risk of sudden cardiac death, for which ICDs and quinidine are potential therapies.
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