Key result
Surgical repair is performed in ~54% of adult ARCAPA cases, favored for symptomatic patients.
Why the study?
ARCAPA is an extremely rare and potentially fatal congenital heart defect, accounting for approximately 0.003% of all coronary artery anomalies.
ARCAPA in adults is a rare, variably presenting congenital anomaly where surgical correction is preferred for symptomatic patients and conservative management with surveillance is acceptable for asymptomatic cases.
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Supports symptom-guided ARCAPA management in adults; leaves open optimal strategy pending prospective studies.
Pereverzeva et al. (2026) conducted a review in Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) (n=59). ARCAPA was evaluated. In a review of 59 adult cases of ARCAPA, surgical correction was performed in 54.2% of patients and conservative management in 40.7%, with surgery preferred for symptomatic patients.
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