What question did this study set out to answer?

To describe a unique case of arrhythmogenic right ventricular cardiomyopathy in an adult with a history of childhood cardiac surgery.

July 17, 2026Cureus0 citationsOpen Access

Atypical Late Presentation of Arrhythmogenic Right Ventricular Cardiomyopathy in a Patient With a History of Childhood Cardiac Surgery

Q: What is the clinical evidence from this study?

Study design: Case Report. Population: Arrhythmogenic right ventricular cardiomyopathy (ARVC) (n=1). Intervention: Multi-modal imaging.

AKAdel Kenawi HAHatem Abdelnasser AMAyman El Masri

Key Result

Multi-modal imaging and the Padua 2020 criteria successfully identified arrhythmogenic right ventricular cardiomyopathy in a 53-year-old man with prior childhood cardiac surgery.

Key Points

To describe a unique case of arrhythmogenic right ventricular cardiomyopathy in an adult with a history of childhood cardiac surgery.
Clinical presentation included dizziness and broad complex tachycardia.
Cardiac imaging utilized to identify features of arrhythmogenic right ventricular cardiomyopathy.
Padua 2020 criteria applied to assess diagnosis in the context of prior congenital heart disease.
Patient exhibited classical features of ARVC: right ventricular dilation, multiple aneurysms, and non-ischemic fibrosis.
Case emphasizes the need for multi-modal imaging in diagnostic processes.
Challenges in distinguishing primary ARVC from alterations due to previous surgery were highlighted.

Study Design

Type

Case Report (n=1)

PICO

Population

A 53-year-old man with a history of childhood cardiac surgery presenting with dizziness and broad complex tachycardia.

Exposure / Comparator

Multi-modal imaging

Limitations

Limited details about the childhood operation.

Abstract

We report a case of a 53-year-old man with a history of childhood cardiac surgery, presenting with dizziness and broad complex tachycardia. Cardiac imaging revealed classical features of arrhythmogenic right ventricular cardiomyopathy (ARVC), including right ventricular dilation, multiple aneurysms, and non-ischemic fibrosis. There is not much information about the details of his childhood operation. This case highlights the diagnostic value of multi-modal imaging and the relevance of the Padua 2020 criteria in identifying arrhythmogenic cardiomyopathy in adults with prior congenital heart disease. This case provides insight into the challenge of distinguishing primary ARVC from remodelling related to previous childhood cardiac surgery, especially when operative details are limited.

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