Key result
Resection and chemotherapy achieve ~2-year survival in primary pulmonary artery chondrosarcoma misdiagnosed as PE.
Why the study?
Primary pulmonary artery chondrosarcoma is an extremely rare tumor that mimics pulmonary embolism, is commonly misdiagnosed, and has few reported studies.
Case Report (n=1)
No
Highlights the critical need to consider pulmonary artery sarcoma in patients with suspected pulmonary embolism who lack PE triggers and respond poorly to anticoagulation, facilitating early diagnosis and surgical intervention.
Background: Primary pulmonary artery sarcoma (PAS) is a rare tumor that presents like pulmonary embolism (PE), primary chondrosarcoma in the pulmonary artery is even rarer and few studies have been reported. PAS are commonly misinterpreted as in a clinical setting, many patients initially receive anticoagulant and thrombolysis therapy, but failed to respond. Management of this condition is difficult and prognosis is poor. We report a case of primary pulmonary artery chondrosarcoma that was initially misdiagnosed as PE and Inappropriate interventional therapy was performed, but with poor response. Finally, patient received surgical treatment, postoperative pathology confirmed primary pulmonary artery chondrosarcoma. Case Description: recurrence of pulmonary artery tumors in 10 months after surgery and received six cycles of adjuvant chemotherapy. The lesions progressed slowly after chemotherapy. The patient subsequently developed lung metastasis in 22 months and died of heart failure and respiratory failure 2 years after surgery. Conclusions: PAS is an extremely rare and the clinical symptoms and radiological features often mimics PE, therefore When doctors make differential diagnosis of pulmonary artery mass lesions, especially when the anticoagulation and thrombolytic effects are very poor. They need to be alert to the possibility of PAS so that early diagnosis and early treatment can prolong the survival of patients.
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Zhang et al. (2023) conducted a case report in Primary pulmonary artery chondrosarcoma (n=1). Pulmonary artery tumor resection, endarterectomy, pulmonary arterioplasty, and adjuvant chemotherapy was evaluated.
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