Key result
Modern echocardiography and sensitive ultrasound techniques have demonstrated mild primary myocardial impairment in patients with Marfan syndrome, supporting the addition of biventricular assessment.
Why the study?
Does modern echocardiography detect primary myocardial impairment in patients with Marfan syndrome?
Does modern echocardiography detect primary myocardial impairment in patients with Marfan syndrome?
Modern echocardiography reveals mild primary myocardial impairment in Marfan syndrome, suggesting biventricular function assessment should be routine alongside aortic root evaluation.
Supports myocardial involvement in Marfan syndrome via sensitive echo; leaves open clinical relevance and need for validation.
Use of echocardiography has dramatically changed the way in which patients with Marfan syndrome are diagnosed, monitored and treated. Owing to the lethal nature of aortic complications, priority has been given to the assessment of the aortic root. Echocardiographic studies on patients with Marfan syndrome have also provided data supporting primary myocardial involvement, although this evidence has remained controversial for several years. Use of more sensitive ultrasound techniques has demonstrated mild myocardial impairment in these patients. Biventricular function assessment should be added to the aortic root evaluation, so that appropriate treatment may be offered to support myocardial function.
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Kiotsekoglou et al. (2009) conducted a review in Marfan syndrome. Modern echocardiography was evaluated. Modern echocardiography and sensitive ultrasound techniques have demonstrated mild primary myocardial impairment in patients with Marfan syndrome, supporting the addition of biventricular assessment.
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