Key result
A 38-year-old man with pulmonary artery intimal sarcoma achieved prolonged survival of 22 months following surgical resection and multiple lines of chemotherapy.
Why the study?
Pulmonary artery intimal sarcoma is an extremely rare and aggressive tumor with a very poor prognosis and median overall survival between 11 and 18 months.
Case Report (n=1)
This case report highlights that aggressive multimodal treatment including surgery and chemotherapy can lead to prolonged survival in patients with extremely rare and aggressive pulmonary artery intimal sarcoma.
Pulmonary artery intimal sarcoma (PAIS) is an extremly rare and agressive tumor. The prognosis is very poor, with median overall survival between 11 and 18 months. We report a case of a 38 year old man who presented to our oncology department with diagnosis of PAIS confirmed by histological examination after surgical resection and bioprosthetic pulmonary valve replacement. Six months after adjuvant chemotherapy, the patient presented a recurrence of his disease that requires other lines of chemotherapy with prolonged survival.
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Khmamouche et al. (2021) conducted a case report in Pulmonary Artery Intimal Sarcoma (n=1). Surgical resection and adjuvant chemotherapy was evaluated on Survival. A 38-year-old man with pulmonary artery intimal sarcoma achieved prolonged survival of 22 months following surgical resection and multiple lines of chemotherapy.
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