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October 1, 1980Archives of Neurology

Pathologic Findings in Mucopolysaccharidosis Type IIIB (Sanfilippo's Syndrome B)

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Authors

MHMichael G.‏ HadfieldUniversity of Hawaiʻi at MānoaNGNitya R. GhatakVirginia Commonwealth University Medical CenterINI. NakonecznaVirginia Commonwealth University Medical Center

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Hadfield et al. (1980) studied this question.

synapsesocial.com/papers/6a7121b635aa2c282ce27274https://doi.org/10.1001/archneur.1980.00500590069012
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Also Consider

Synapse has enriched 4 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1NEUROCHEMISTRY OF THE MUCOPOLYSACCHARIDOSES: BRAIN GLYCOSAMINOGLYCANS, LIPIDS AND LYSOSOMAL ENZYMES IN MUCOPOLYSACCHARIDOSIS TYPE III B (α‐N‐ACETYLGLUCOSAMINIDASE DEFICIENCY)1978 · 31 citations
  2. 2Neuropathology of sanfilippo syndrome1977 · 19 citations
  3. 3MUCOPOLYSACCHARIDOSIS TYPE III (SANFILIPPO'S SYNDROME)1971 · 17 citations
  4. 4Clinical variability in Sanfilippo B disease: a report on six patients in two related sibships1976 · 30 citations