Giant sacral schwannoma mimicking teratoma

Background: Sacral schwannomas are uncommon, constituting 1-5% of schwannomas. They present with vague symptoms. Schwannomas occurring in sacral and presacral regions present with enormous dimensions and are difficult to manage. Case summary: We present a case of schwannoma occurring in the sacral region extending into the presacral region in a 45-year-old female which was diagnosed as teratoma on imageology. The lesion was excised and on histopathological examination, diagnosis of schwannoma was considered Conclusion: Sacral schwannoma with cystic degeneration should be considered as a differential diagnosis for solid and cystic lesions of the sacral region. MRI and CT scanning will be helpful in diagnosis.