Why the study?
Is intrapericardial ICD implantation feasible in young children with a high risk for sudden cardiac death?
Is intrapericardial ICD implantation feasible in young children with a high risk for sudden cardiac death?
Intrapericardial ICD implantation is feasible in young children at high risk for sudden cardiac death, though underlying disease progression remains a challenge.
Supports feasibility of intrapericardial ICD in young children; leaves open survival impact amid DCM progression.
Cardiac sodium channel dysfunction associated with the SCN5A gene presents with mixed phenotypes, including long QT syndrome type 3, sinus node dysfunction, and dilated cardiomyopathy (DCM). We report a Korean case of an overlap syndrome of cardiac sodium channelopathy with SCN5A p.R1193Q polymorphism, treated by the placement of an intrapericardial implantable cardioverter-defibrillator (ICD) at the age of 27 months. Although the patient received two appropriate life-saving shocks for ventricular fibrillations, he eventually died of DCM progression. However, this case shows that intrapericardial ICD implantation is feasible in young children with a high risk for sudden cardiac death.
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Kwon et al. (2012) studied this question.
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