Primary mediastinal liposarcoma in children is a rare and aggressive tumor with poor prognosis despite surgery and chemotherapy.
Case report of rapid recurrence and death underscores poor prognosis in pediatric mediastinal liposarcoma; leaves open optimal management for this rare entity.
A case of primary anterior mediastinal liposarcoma occurring in a child is reported. A 5-year-old male child complained of exertional dyspnea and left chestpain. The chest roentgenogram showed a complete opacity of the left pleural space. After thoracotomy, the histological examination revealed mediastinal myxoid-pleomorphic liposarcoma. Surgical resection was performed and chemotherapy was given; 10 months later a recurrence was noted in the mediastinum. The child died 17 months after establishing the diagnosis.
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Plukker et al. (1988) studied this question.
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