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Extraluminal growth predominates in IVC leiomyosarcoma; extends descriptive data but leaves open management implications.
Primary vascular leiomyosarcoma is a rare tumor that arises mainly from the inferior vena cava (IVC). It is usually a slow-growing progressive tumor. It shows mainly three type of growth patterns; 62% of cases demonstrate extraluminal pattern, 5% cases show intraluminal pattern, and 33% extra- and intraluminal growth patterns.
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Dave et al. (2020) studied this question.
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